Purpura-associated congenital lymphedema
Identifieur interne : 006800 ( Main/Exploration ); précédent : 006799; suivant : 006801Purpura-associated congenital lymphedema
Auteurs : Samantha Berti [Italie] ; Alessandro Pieri [Italie] ; Torello Lotti [Italie] ; Alberto Duranti [Italie] ; John Panelos [Italie] ; Maurizio De Martino [Italie] ; Silvia Moretti [Italie]Source :
- EJD. European journal of dermatology [ 1167-1122 ] ; 2009.
Descripteurs français
- Pascal (Inist)
English descriptors
- KwdEn :
Abstract
An 8-year-old girl referred to our Department for a two-month worsening of congenital primary lymphedema of the lower limb and for the appearance of several purpuric lesions on the right thigh and knee. We diagnosed a lichenoid pigmented purpura of Gougerot and Blum in a patient with Milroy disease, complicated by an insufficiency of anterior saphena. We treated the patient with topical steroids and compression stockings, until surgical intervention of phlebectomy. We report this case for the rarity of the disease, for the even more rare association with lichenoid pigmented purpura and for cutaneous immunopathological findings.
Affiliations:
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Le document en format XML
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sortKey="Lotti, Torello" sort="Lotti, Torello" uniqKey="Lotti T" first="Torello" last="Lotti">Torello Lotti</name><affiliation wicri:level="1"><inist:fA14 i1="03"><s1>Department of Dermatology, University of Florence</s1><s2>Florence</s2><s3>ITA</s3><sZ>3 aut.</sZ><sZ>7 aut.</sZ></inist:fA14><country>Italie</country><wicri:noRegion>Florence</wicri:noRegion></affiliation></author><author><name sortKey="Duranti, Alberto" sort="Duranti, Alberto" uniqKey="Duranti A" first="Alberto" last="Duranti">Alberto Duranti</name><affiliation wicri:level="1"><inist:fA14 i1="01"><s1>Department of Pediatric Medicine, Anna Meyer Children's Hospital, Viale Pieraccini, 24</s1><s2>50132 Florence</s2><s3>ITA</s3><sZ>1 aut.</sZ><sZ>4 aut.</sZ><sZ>6 aut.</sZ></inist:fA14><country>Italie</country><wicri:noRegion>50132 Florence</wicri:noRegion></affiliation></author><author><name sortKey="Panelos, John" sort="Panelos, John" uniqKey="Panelos J" first="John" last="Panelos">John Panelos</name><affiliation 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level="a">Purpura-associated congenital lymphedema</title><author><name sortKey="Berti, Samantha" sort="Berti, Samantha" uniqKey="Berti S" first="Samantha" last="Berti">Samantha Berti</name><affiliation wicri:level="1"><inist:fA14 i1="01"><s1>Department of Pediatric Medicine, Anna Meyer Children's Hospital, Viale Pieraccini, 24</s1><s2>50132 Florence</s2><s3>ITA</s3><sZ>1 aut.</sZ><sZ>4 aut.</sZ><sZ>6 aut.</sZ></inist:fA14><country>Italie</country><wicri:noRegion>50132 Florence</wicri:noRegion></affiliation></author><author><name sortKey="Pieri, Alessandro" sort="Pieri, Alessandro" uniqKey="Pieri A" first="Alessandro" last="Pieri">Alessandro Pieri</name><affiliation wicri:level="1"><inist:fA14 i1="02"><s1>Department of Cardiology, University of Florence</s1><s2>Florence</s2><s3>ITA</s3><sZ>2 aut.</sZ></inist:fA14><country>Italie</country><wicri:noRegion>Florence</wicri:noRegion></affiliation></author><author><name sortKey="Lotti, Torello" sort="Lotti, Torello" uniqKey="Lotti T" first="Torello" last="Lotti">Torello Lotti</name><affiliation wicri:level="1"><inist:fA14 i1="03"><s1>Department of Dermatology, University of Florence</s1><s2>Florence</s2><s3>ITA</s3><sZ>3 aut.</sZ><sZ>7 aut.</sZ></inist:fA14><country>Italie</country><wicri:noRegion>Florence</wicri:noRegion></affiliation></author><author><name sortKey="Duranti, Alberto" sort="Duranti, Alberto" uniqKey="Duranti A" first="Alberto" last="Duranti">Alberto Duranti</name><affiliation wicri:level="1"><inist:fA14 i1="01"><s1>Department of Pediatric Medicine, Anna Meyer Children's Hospital, Viale Pieraccini, 24</s1><s2>50132 Florence</s2><s3>ITA</s3><sZ>1 aut.</sZ><sZ>4 aut.</sZ><sZ>6 aut.</sZ></inist:fA14><country>Italie</country><wicri:noRegion>50132 Florence</wicri:noRegion></affiliation></author><author><name sortKey="Panelos, John" sort="Panelos, John" uniqKey="Panelos J" first="John" last="Panelos">John Panelos</name><affiliation wicri:level="1"><inist:fA14 i1="04"><s1>Department of Human Oncology and Pathology, University of Florence</s1><s2>Florence</s2><s3>ITA</s3><sZ>5 aut.</sZ></inist:fA14><country>Italie</country><wicri:noRegion>Florence</wicri:noRegion></affiliation></author><author><name sortKey="De Martino, Maurizio" sort="De Martino, Maurizio" uniqKey="De Martino M" first="Maurizio" last="De Martino">Maurizio De Martino</name><affiliation wicri:level="1"><inist:fA14 i1="01"><s1>Department of Pediatric Medicine, Anna Meyer Children's Hospital, Viale Pieraccini, 24</s1><s2>50132 Florence</s2><s3>ITA</s3><sZ>1 aut.</sZ><sZ>4 aut.</sZ><sZ>6 aut.</sZ></inist:fA14><country>Italie</country><wicri:noRegion>50132 Florence</wicri:noRegion></affiliation></author><author><name sortKey="Moretti, Silvia" sort="Moretti, Silvia" uniqKey="Moretti S" first="Silvia" last="Moretti">Silvia Moretti</name><affiliation wicri:level="1"><inist:fA14 i1="03"><s1>Department of Dermatology, University of Florence</s1><s2>Florence</s2><s3>ITA</s3><sZ>3 aut.</sZ><sZ>7 aut.</sZ></inist:fA14><country>Italie</country><wicri:noRegion>Florence</wicri:noRegion></affiliation></author></analytic><series><title level="j" type="main">EJD. European journal of dermatology</title><title level="j" type="abbreviated">EJD, Eur. j. dermatol.</title><idno type="ISSN">1167-1122</idno><imprint><date when="2009">2009</date></imprint></series></biblStruct></sourceDesc><seriesStmt><title level="j" type="main">EJD. European journal of dermatology</title><title level="j" type="abbreviated">EJD, Eur. j. dermatol.</title><idno type="ISSN">1167-1122</idno></seriesStmt></fileDesc><profileDesc><textClass><keywords scheme="KwdEn" xml:lang="en"><term>Congenital</term><term>Dermatology</term><term>Genetic disease</term><term>Lymphedema</term><term>Purpura</term><term>Saphenous vein</term><term>Ulceration</term></keywords><keywords scheme="Pascal" xml:lang="fr"><term>Purpura</term><term>Lymphoedème</term><term>Maladie héréditaire</term><term>Congénital</term><term>Veine saphène</term><term>Ulcération</term><term>Dermatologie</term></keywords></textClass></profileDesc></teiHeader><front><div type="abstract" xml:lang="en">An 8-year-old girl referred to our Department for a two-month worsening of congenital primary lymphedema of the lower limb and for the appearance of several purpuric lesions on the right thigh and knee. We diagnosed a lichenoid pigmented purpura of Gougerot and Blum in a patient with Milroy disease, complicated by an insufficiency of anterior saphena. We treated the patient with topical steroids and compression stockings, until surgical intervention of phlebectomy. We report this case for the rarity of the disease, for the even more rare association with lichenoid pigmented purpura and for cutaneous immunopathological findings.</div></front></TEI><affiliations><list><country><li>Italie</li></country></list><tree><country name="Italie"><noRegion><name sortKey="Berti, Samantha" sort="Berti, Samantha" uniqKey="Berti S" first="Samantha" last="Berti">Samantha Berti</name></noRegion><name sortKey="De Martino, Maurizio" sort="De Martino, Maurizio" uniqKey="De Martino M" first="Maurizio" last="De Martino">Maurizio De Martino</name><name sortKey="Duranti, Alberto" sort="Duranti, Alberto" uniqKey="Duranti A" first="Alberto" last="Duranti">Alberto Duranti</name><name sortKey="Lotti, Torello" sort="Lotti, Torello" uniqKey="Lotti T" first="Torello" last="Lotti">Torello Lotti</name><name sortKey="Moretti, Silvia" sort="Moretti, Silvia" uniqKey="Moretti S" first="Silvia" last="Moretti">Silvia Moretti</name><name sortKey="Panelos, John" sort="Panelos, John" uniqKey="Panelos J" first="John" last="Panelos">John Panelos</name><name sortKey="Pieri, Alessandro" sort="Pieri, Alessandro" uniqKey="Pieri A" first="Alessandro" last="Pieri">Alessandro Pieri</name></country></tree></affiliations></record>Pour manipuler ce document sous Unix (Dilib)
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